/thymoma type A

thymoma type A

Rare Disease

MONDO:0002588

Also Known As

medullary thymomaprimary thymic epithelial neoplasm type Aprimary thymic epithelial tumor type Aprimary thymic epithelial tumour type Aspindle cell thymomathymoma type Athymoma, medullary

Definition

A thymic epithelial neoplasm characterized by the presence of spindle and/or oval neoplastic epithelial cells. Lymphocytic infiltration is minimal or absent. It may be associated with myasthenia gravis or pure red cell aplasia. The majority of cases occur in the anterior mediastinum as Masaoka stage I tumors. Approximately 20% of the cases occur as stage II or stage III tumors. Type A thymoma generally behaves as a benign tumor and the overall survival is reported to be 100% at 5 and 10 years.