/clear cell sarcoma

clear cell sarcoma

Rare Disease

MONDO:0002926

Also Known As

adult soft part clear cell sarcomachordoid sarcomaclear cell sarcoma (morphologic abnormality)clear cell sarcoma - not kidneyclear cell sarcoma of soft partsclear cell sarcoma of soft tissueclear cell sarcoma/malignant melanoma of soft parts (excluding clear cell sarcoma of the kidney)malignant melanoma of soft tissuesmalignant melanoma of the soft partsmelanoma, malignant, of soft partsmalignant melanoma of soft parts

Definition

A rare malignant neoplasm with melanocytic differentiation characterized by the presence of polygonal or spindle shaped clear cells. This sarcoma usually affects the tendons and aponeuroses and is associated with a poor prognosis due to recurrences and metastases.