/hereditary Wilms tumor

hereditary Wilms tumor

Rare Disease

MONDO:0003321

Also Known As

familial Wilms tumorfamilial Wilms tumourfamilial Wilms' tumorfamilial Wilms' tumourhereditary Wilms tumorhereditary Wilms' tumorhereditary Wilms' tumourhereditary kidney adenosarcomahereditary nephroblastomahereditary renal adenosarcomaWT1

Definition

Familial embryonal neoplasm derived from nephrogenic blastemal cells. Several lines of differentiation, including blastemal, stromal and epithelial, are usually expressed. Comprises approximately 1% of Wilms tumors. (AFIP fascicle version 2.0)