/ampulla of vater small cell neuroendocrine carcinoma

ampulla of vater small cell neuroendocrine carcinoma

Rare Disease

MONDO:0004117

Also Known As

ampulla of Vater small cell NECampulla of Vater small cell carcinomaampulla of Vater small cell neuroendocrine carcinomaampullary small cell carcinomahepatopancreatic ampulla small cell carcinomasmall cell neuroendocrine carcinoma of the ampullary region

Definition

An aggressive neuroendocrine carcinoma arising from the ampulla of Vater and the periampullary region. Morphologically, it is characterized by the presence of small malignant cells, necrosis, and a high mitotic rate. Signs and symptoms include jaundice, abdominal pain, anorexia, nausea, vomiting, and weight loss.