/lymphoepithelioma-like thymic carcinoma

lymphoepithelioma-like thymic carcinoma

Rare Disease

MONDO:0004297

Also Known As

lymphoepithelial Thymus cancerlymphoepithelial cancer of Thymuslymphoepithelial cancer of the Thymuslymphoepithelioma-like Thymus carcinomalymphoepithelioma-like carcinoma of Thymuslymphoepithelioma-like carcinoma of the Thymuslymphoepithelioma-like thymic carcinomamalignant lymphoepithelial thymomathymic lymphoepithelioma-like carcinoma

Definition

A rare, usually aggressive primary thymic carcinoma, characterized by a syncytial growth of undifferentiated carcinoma cells and the presence of a lymphoplasmacytic infiltrate. More than 40% of cases are associated with Epstein-Barr virus infection.