/primary biliary cholangitis

primary biliary cholangitis

Rare Disease

MONDO:0005388

Also Known As

Hanot syndromePBCbiliary liver cirrhosischolestatic cirrhosischronic non-suppurative destructive cholangitischronic nonsuppurative destructive cholangitisprimary Bilary cirrhosis (PBC)primary biliary cirrhosisbiliary cirrhosis, primaryfamilial primary biliary cirrhosis

Definition

Primary biliary cholangitis (PBC) is a chronic and slowly progressive cholestatic liver disease of autoimmune etiology characterized by injury of the intrahepatic bile ducts that may eventually lead to liver failure.