/fibrolamellar hepatocellular carcinoma

fibrolamellar hepatocellular carcinoma

Rare Disease

MONDO:0006210

Also Known As

FHCCFLCfibrolamellar cancerfibrolamellar carcinomafibrolamellar carcinoma of liver cellsfibrolamellar carcinoma of the liver cellsfibrolamellar hepatocarcinomafibrolamellar hepatocellular carcinomahepatocellular carcinoma, fibrolamellarhepatocellular fibrolamellar carcinomaliver cell fibrolamellar carcinomaoncocytic hepatocellular tumoroncocytic hepatocellular tumourpolygonal cell type hepatocellular carcinoma with fibrous StromaFL-HCCeosinophilic glassy cell hepatomaeosinophilic hepatocellular carcinoma with lamellar fibrosisfibrolamellar oncocytic hepatomafibrolamellar variant of hepatocellular carcinomahepatocellular carcinoma (fibrolamellar variant)hepatocellular carcinoma with increased stromal fibrosispolygonal cell hepatocellular carcinoma with fibrous stroma

Definition

A distinctive type of liver cell carcinoma that arises in non-cirrhotic livers and is seen predominantly in young patients. The tumor cells are polygonal and deeply eosinophilic, and are embedded in a fibrous stroma. The prognosis is similar to classical hepatocellular carcinoma that arises in non-cirrhotic livers, and better than hepatocellular carcinoma that arises in cirrhotic livers.