/prune belly syndrome

prune belly syndrome

Rare Disease

MONDO:0007032

Also Known As

Obrinsky syndromeObrisnksy syndromeabdominal muscle deficiency syndromeeagle-Barret syndromeprune belly syndromesyndrome of agenesis of abdominal musclestriad syndromePBSabdominal muscles, absence of, with urinary tract Abnormality and cryptorchidismeagle-Barrett syndrome

Definition

Prune belly syndrome is a rare congenital disorder, belonging to the group of fetal lower urinary tract obstructions (LUTO), involving variable dilation of the lower urinary tract in association with partial or complete absence of the lateral and inferior abdominal wall musculature and in males bilateral non-palpable undescended testes.