/dentinogenesis imperfecta type 3

dentinogenesis imperfecta type 3

Rare Disease

MONDO:0007442

Also Known As

DGI-IIIDentinogenesis Imperfecta Type IIIbrandywine type dentinogenesis imperfectadentinogenesis imperfecta Shields type 3dentinogenesis imperfecta type IIIdentinogenesis imperfecta, Shields type 3dentinogenesis imperfecta, Shields type III

Definition

Dentinogenesis imperfecta type 3 (DGI-3) is a rare, severe form of dentinogenesis imperfecta (DGI) characterized by opalescent primary and permanent teeth, marked attrition, large pulp chambers, multiple pulp exposure and shell teeth radiographically (i.e. teeth which appear hollow due to dentin hypotrophy).