/desquamative interstitial pneumonia

desquamative interstitial pneumonia

Rare Disease

MONDO:0009887

Also Known As

RBILDdesquamative interstitial pneumoniafamilial desquamative interstitial pneumonitisrespiratory bronchiolitis interstitial lung diseaserespiratory bronchiolitis-associated interstitial lung diseaseDIPILD, desquamativeinterstitial lung disease, desquamativeinterstitial pneumonitis, desquamative, familialpneumonia, desquamative interstitial, familialpneumonitis, desquamative interstitial, familial

Definition

A rare idiopathic interstitial pneumonia characterized by accumulation of macrophages in alveolar spaces and interstitial inflammation. It usually occurs in smokers. Some patients develop progressive interstitial lung fibrosis.