/generalized peeling skin syndrome

generalized peeling skin syndrome

Rare Disease

MONDO:0010033

Also Known As

generalised PSSgeneralised deciduous skingeneralized PSSgeneralized deciduous skinpeeling skin syndrome type 1PSS1peeling skin syndrome 1

Definition

Generalized peeling skin syndrome (PSS) is a form of PSS presenting with a generalized distribution. It comprises two sub-types: the non-inflammatory (PSS type A) and the inflammatory (PSS type B) form. PSS type A is characterized by generalized white scaling with superficial peeling of the skin, while PSS type B is characterized by superficial patchy peeling of the entire skin with underlying erythroderma, associated with pruritus, and atopy.