/Thiel-Behnke corneal dystrophy

Thiel-Behnke corneal dystrophy

Rare Disease

MONDO:0011185

Also Known As

TBCDThiel-Behnke corneal dystrophyWaardenburg-Jonker corneal dystrophyanterior limiting membrane dystrophy type 2anterior limiting membrane dystrophy type IIcorneal dystrophy honeycomb-shapedcorneal dystrophy of Bowman layer type 2corneal dystrophy of Bowman layer type IIcurly fiber corneal dystrophycurly fibre corneal dystrophyhoneycomb corneal dystrophyCDB2CDTBThiel Behnke corneal dystrophycorneal dystrophy Thiel Behnke typecorneal dystrophy honeycomb shapedcorneal dystrophy of Bowman Layer, type 2corneal dystrophy of the Bowman layer type 2corneal dystrophy, Thiel-Behnke typecorneal dystrophy, honeycomb-Shaped

Definition

Thiel-Behnke corneal dystrophy (TBCD) is a rare form of superficial corneal dystrophy characterized by sub-epithelial honeycomb-shaped corneal opacities in the superficial cornea, and progressive visual impairment.