Hereditary North American Indian childhood cirrhosis is a severe autosomal recessive intrahepatic cholestasis that has only been described in aboriginal children from northwestern Quebec. Manifesting first as transient neonatal jaundice, the disease evolves into periportal fibrosis and cirrhosis during a period ranging from childhood to adolescence.
Comprehensive, easy-to-understand information about this condition
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progressive familial intrahepatic cholestasis type 1
MONDO:0008892
benign recurrent intrahepatic cholestasis type 1
MONDO:0009469
progressive familial intrahepatic cholestasis type 2
MONDO:0011156
progressive familial intrahepatic cholestasis type 3
MONDO:0011214
cholestasis, progressive familial intrahepatic, 4
MONDO:0014381
cholestasis, progressive familial intrahepatic, 5
MONDO:0014884