/familial acute necrotizing encephalopathy

familial acute necrotizing encephalopathy

Rare Disease

MONDO:0011953

Also Known As

ADANEencephalopathy, acute, infection-induced, 3, susceptibility toencephalopathy, acute, infection-induced, susceptibility to, type 3recurrent acute necrotizing encephalopathyANE1IIAE3Postinfectious acute necrotizing hemorrhagic encephalopathyacute necrotizing encephalopathy type 1autosomal dominant acute necrotizing encephalopathyencephalopathy, acute necrotizing, susceptibility toencephalopathy, acute, infection-induced, susceptibility to, 3infection-induced acute encephalopathy 3susceptibility to acute infection-induced encephalopathy-3susceptibility to acute necrotizing encephalopathysusceptibility to infection-induced acute encephalopathy 3

Definition

Familial acute necrotizing encephalopathy or ADANE is a potentially fatal neurological disease characterized by neuropathological lesions principally involving the brainstem, thalamus and putamen.