/Ewing sarcoma

Ewing sarcoma

Rare Disease

MONDO:0012817

Also Known As

ESEwing sarcomaEwing's family localised tumourEwing's family localized tumorEwing's sarcomaEwing's tumorEwing's tumourEwings sarcomaPNET of Thoracopulmonary regionEwing tumorEwing tumourEwing's sarcoma/peripheral primitive neuroectodermal tumourEwings sarcoma-primitive neuroectodermal tumorEwings sarcoma-primitive neuroectodermal tumourlocalised Ewing sarcomalocalised Ewing's sarcomalocalised Ewing's sarcoma/peripheral primitive neuroectodermal tumourlocalised Ewing's tumourlocalised peripheral primitive neuroectodermal tumourlocalized Ewing sarcomalocalized Ewing's sarcomalocalized Ewing's sarcoma/peripheral primitive neuroectodermal tumorlocalized Ewing's tumorlocalized peripheral primitive neuroectodermal tumorneuroepitheliomaneuroepithelioma, peripheralperipheral primitive neuroectodermal tumoursarcoma, Ewing's

Definition

A small round cell tumor that lacks morphologic, immunohistochemical, and electron microscopic evidence of neuroectodermal differentiation. It represents one of the two ends of the spectrum called Ewing sarcoma/peripheral neuroectodermal tumor. It affects mostly males under age 20, and it can occur in soft tissue or bone. Pain and the presence of a mass are the most common clinical symptoms.