Primary sclerosing cholangitis (PSC) is a rare, slowly progressive liver disease characterized by inflammation and destruction of the intra- and/or extra-hepatic bile ducts that lead to cholestasis, liver fibrosis, liver cirrhosis and ultimately liver failure.
Comprehensive, easy-to-understand information about this condition
Checking for content...
nephropathy, progressive tubulointerstitial, with cholestatic liver disease
MONDO:0011199
neonatal ichthyosis-sclerosing cholangitis syndrome
MONDO:0011874
IgG4-related sclerosing cholangitis
MONDO:0018645
secondary sclerosing cholangitis
MONDO:0018647
isolated neonatal sclerosing cholangitis
MONDO:0018816