/primary cutaneous amyloidosis

primary cutaneous amyloidosis

Rare Disease

MONDO:0015301

Also Known As

primary localised cutaneous amyloidosisprimary localized cutaneous amyloidosisPLCAfamilial primary localised cutaneous amyloidosisfamilial primary localized cutaneous amyloidosisamyloidosis IXamyloidosis familial cutaneous lichenamyloidosis, primary localised cutaneousamyloidosis, primary localized cutaneouslichen amyloidosis familial

Definition

Cutaneous amyloidosis refers to a variety of skin diseases characterized histologically by the extracellular accumulation of amyloid deposits in the dermis. Rare forms include lichen amyloidosus, X-linked reticulate pigmentary disorder, primary localized cutaneous nodular amyloidosis, and macular amyloidosis.