Also Known As
CSSChurg Strauss SyndromeChurg Strauss syndromeChurg-Strauss syndromeChurg-Strauss vasculitisEGPAallergic angiitidesallergic angiitides, granulomatousallergic angiitisallergic angiitis and granulomatosisallergic angiitis, granulomatousallergic granulomatosesallergic granulomatosisallergic granulomatosis angiitisallergic granulomatous Angiitidesallergic granulomatous and angiitisallergic granulomatous angiitisangiitides, allergicangiitides, allergic granulomatousangiitides, granulomatous allergicangiitis, allergicangiitis, allergic granulomatousangiitis, granulomatous allergiceosinophilic granulomatous Vasculitideseosinophilic granulomatous vasculitisgranulomatoses, allergicgranulomatosis, allergicgranulomatous allergic Angiitidesgranulomatous allergic angiitisgranulomatous angiitides, allergicgranulomatous angiitis, allergicgranulomatous vasculitides, eosinophilicgranulomatous vasculitis, eosinophilicsyndrome, Churg-Straussvasculitides, eosinophilic granulomatousvasculitis, Churg Straussvasculitis, Churg-Straussvasculitis, eosinophilic granulomatous
Definition
Eosinophilic granulomatosis with polyangiitis (EGPA), previously known as Churg-Strauss syndrome, is a systemic vasculitis of small-to medium vessels, characterized by asthma, transient pulmonary infiltrates, and hypereosinophilia.