/hereditary gingival fibromatosis

hereditary gingival fibromatosis

Rare Disease

MONDO:0016070

Also Known As

autosomal dominant gingival fibromatosisautosomal dominant gingival hyperplasiahereditary gingival fibromatosishereditary gingival hyperplasia

Definition

Hereditary gingival fibromatosis (HGF) is a rare benign, slowly progressive, non-inflammatory fibrous hyperplasia of the maxillary and mandibular gingivae that generally occurs with the eruption of the permanent (or more rarely the primary) dentition or even at birth. It presents as a localized or generalized, smooth or nodular overgrowth of the gingival tissues of varying severity. It can be isolated, with autosomal dominant inheritance, or as part of a syndrome.