/solitary fibrous tumor

solitary fibrous tumor

Rare Disease

MONDO:0016238

Also Known As

SFTlocalised fibrous mesotheliomalocalised fibrous tumourlocalized fibrous mesotheliomalocalized fibrous tumorsolitary fibrous tumorsubmesothelial fibromahemangiopericytomasolitary fibrous tumor/hemangiopericytoma

Definition

Solitary fibrous tumor (SFT) represents a diverse group of ubiquitous rare spindle cell neoplasms that may be benign or malignant and that most frequently arises from the pleura and peritoneum and rarely from other sites such as head and neck, liver and skeletal muscle. SFT may be clinically asymptomatic or may present with enlarging mass, compressive effects depending on the site involved and rarely with paraneoplastic manifestations (osteoarthropathy or hypoglycemia).