/primitive neuroectodermal tumor of the cervix uteri

primitive neuroectodermal tumor of the cervix uteri

Rare Disease

MONDO:0016284

Also Known As

cervical malignant peripheral neuroectodermal tumorcervical malignant peripheral neuroectodermal tumourcervical peripheral neuroectodermal cancermalignant peripheral neuroectodermal tumor of the cervix uterimalignant peripheral neuroectodermal tumour of the cervix uteriperipheral neuroectodermal cancer of cervix uteri

Definition

Primitive neuroectodermal tumor of the cervix uteri is a rare cancer of cervix uteri derived from neural crest cells, histologically composed of small, round neoplatic cells with variable degree of neural, glial and ependymal differentiation. Macroscopically, the tumor is often a large, soft, poorly circumscribed mass with infiltrative borders and necrotic areas. It presents with dysfunctional vaginal bleeding or discharge, lower abdominal pain and uterine enlargement.