Postlingual non-syndromic genetic deafness is a rare, genetically highly heterogeneous otorhinolaryngologic disease, resulting from inner and/or middle ear or hearing nerve anomalies, typically characterized by progressive, bilateral, moderate to profound hearing loss (mean sensorineural hearing impairment equal to 40 dB or more for 500-, 1,000-, and 2,000-Hz frequency tones in the better ear) which occurs after the onset of speech development and is not associated with visible external ear abnormalities or any other medical problems. Language development is not initially significantly delayed.
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deafness, aminoglycoside-induced
MONDO:0010799
prelingual non-syndromic genetic hearing loss
MONDO:0016297
X-linked nonsyndromic hearing loss
MONDO:0019586
autosomal dominant nonsyndromic hearing loss
MONDO:0019587
hearing loss, autosomal recessive
MONDO:0019588
nonsyndromic deafness, Y-linked
MONDO:0033304