/limited systemic sclerosis

limited systemic sclerosis

Rare Disease

MONDO:0016359

Also Known As

SSC without skin involvementsystemic sclerosis sine sclerodermasystemic sclerosis without skin involvementScleroderma, sineprogressive systemic sclerosis sine scleroderma

Definition

Limited systemic sclerosis (lSSc) (or SSc sine scleroderma) is a subset of systemic sclerosis (SSc) characterized by organ involvement in the absence of fibrosis of the skin.