/ganglioglioma

ganglioglioma

Rare Disease

MONDO:0016733

Also Known As

CNS gangliogliomagangliogliomaadult gangliogliomachildhood gangliogliomamixed cell tumors containing both neural ganglionic cells and neural glial cell componentsmixed cell tumours containing both neural ganglionic cells and neural glial cell components

Definition

A well differentiated, slow growing neuroepithelial neoplasm composed of neoplastic, mature ganglion cells and neoplastic glial cells. Some gangliogliomas show anaplastic features in their glial component and are considered to be WHO grade III. Rare cases of newly diagnosed gangliogliomas with grade IV (glioblastoma) changes in the glial component have also been reported. (Adapted from WHO)