/Epstein-Barr virus-positive diffuse large B-cell lymphoma of the elderly

Epstein-Barr virus-positive diffuse large B-cell lymphoma of the elderly

Rare Disease

MONDO:0017346

Also Known As

EBV Positive diffuse large B-cell lymphoma of the elderlyEBV-Positive diffuse large B-cell lymphoma, NOSEBV-positive DLBCL of the elderlyEpstein-Barr Virus Positive diffuse large B-cell lymphoma of the elderlySenile EBV-associated B-cell lymphoproliferative disorderage-related EBV Positive B-cell lymphoproliferative disorder

Definition

A rare form of diffuse large B-cell lymphoma occurring most commonly in patients over the age of 50 (usually between 70-75 years of age), without overt immunodeficiency, and presenting with nodal and extranodal involvement (in sites such as the stomach, lung, skin and pancreas) and B symptoms (fever, night sweats, weight loss). The tumor is characterized by an aggressive course and a short survival rate.