/primary cutaneous anaplastic large cell lymphoma

primary cutaneous anaplastic large cell lymphoma

Rare Disease

MONDO:0017598

Also Known As

ALCL, cutaneousC-ALCLanaplastic large-cell lymphoma, primary cutaneous typeprimary C-ALCLprimary anaplastic large cell lymphoma of skinprimary anaplastic large cell lymphoma of the skinprimary cutaneous CD30 Positive anaplastic large cell lymphomaprimary cutaneous CD30+ ALCLprimary cutaneous CD30+ anaplastic large cell lymphomaregressive atypical histiocytosis

Definition

Primary cutaneous anaplastic large cell lymphoma (C-ALCL) is a rare T-cell non-Hodgkin lymphoma that affects the skin and generally shows no extracutaneous involvement at presentation. It belongs to the spectrum of primary cutaneous CD30+ lymphoproliferative disorders along with lymphomatoid papulosis with which it shares overlapping clinical and histopathologic features.