/Langerhans cell histiocytosis

Langerhans cell histiocytosis

Rare Disease

MONDO:0018310

Also Known As

LCHLangerhan's cell histiocytosisLangerhans cell granulomatosisLangerhans cell histiocytosisLangerhans cell histiocytosis, NOSLangerhans cell histiocytosis, Not otherwise specifiedhistiocytosis Xletterer-Siwe disease involving intra-abdominal lymph nodesletterer-Siwe disease involving intrapelvic lymph nodesletterer-Siwe disease involving intrathoracic lymph nodesletterer-Siwe disease involving lymph nodes of axilla and upper limbletterer-Siwe disease involving lymph nodes of head, face and neckletterer-Siwe disease involving lymph nodes of head, face, and neckletterer-Siwe disease involving lymph nodes of inguinal region and lower limbletterer-Siwe disease involving lymph nodes of multiple sitesletterer-Siwe disease involving spleenletterer-Siwe disease of intra-abdominal lymph nodesletterer-Siwe disease of intrapelvic lymph nodesletterer-Siwe disease of intrathoracic lymph nodesletterer-Siwe disease of lymph nodes of axilla and upper limbletterer-Siwe disease of lymph nodes of axilla and/or upper limbletterer-Siwe disease of lymph nodes of head, face and neckletterer-Siwe disease of lymph nodes of head, face and/or neckletterer-Siwe disease of lymph nodes of inguinal region amd/or lower limbletterer-Siwe disease of lymph nodes of inguinal region and lower limbletterer-Siwe disease of lymph nodes of inguinal region and/or lower limbletterer-Siwe disease of lymph nodes of multiple sitesletterer-Siwe disease of spleenLangerhans-cell histiocytosisLch

Definition

Langerhans cell histiocytosis (LCH) is a systemic disease associated with the proliferation and accumulation (usually in granulomas) of Langerhans cells in various tissues.