/solid pseudopapillary carcinoma of pancreas

solid pseudopapillary carcinoma of pancreas

Rare Disease

MONDO:0018525

Also Known As

solid pseudopapillary neoplasm of the pancreaspancreatic solid pseudopapillary carcinomasolid pseudopapillary carcinoma of pancreassolid pseudopapillary carcinoma of the pancreas

Definition

A malignant neoplasm arising from the exocrine pancreas. It occurs predominantly in young women. It is characterized by the presence of extensive necrosis and hemorrhage and is composed of polyhedral cells forming solid and pseudopapillary patterns. There is morphologic evidence of perineural invasion, vascular invasion, or extensive invasion into the surrounding tissues.