/enteropathy-associated T-cell lymphoma

enteropathy-associated T-cell lymphoma

Rare Disease

MONDO:0019473

Also Known As

EATLEATL, type IETTLenteropathy associated T-cell lymphomaenteropathy-associated T-cell lymphoma, type Ienteropathy-type T-cell lymphomaintestinal T-cell lymphomaEATCLhigh-grade pleomorphic peripheral T-cell lymphoma

Definition

An uncommon mature T-cell lymphoma of intraepithelial lymphocytes. It usually arises from the small intestine, most commonly the jejunum or ileum. Other less frequent primary anatomic sites include the duodenum, stomach, colon, or outside the gastrointestinal tract. It is seen with increased frequency in regions with a high prevalence of celiac disease.