A benign or malignant, usually non-functioning, extra-adrenal paraganglioma that arises from paraganglia located along the parasympathetic nerves. Representative examples include aorticopulmonary, carotid body, jugulotympanic, and mediastinal paragangliomas.
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head and neck paraganglioma
MONDO:0006239
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pheochromocytoma/paraganglioma syndrome 1
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pheochromocytoma/paraganglioma syndrome 2
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pheochromocytoma/paraganglioma syndrome 3
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pheochromocytoma/paraganglioma syndrome 5
MONDO:0013602