/atypical childhood epilepsy with centrotemporal spikes

atypical childhood epilepsy with centrotemporal spikes

Rare Disease

MONDO:0100020

Also Known As

atonic-benign childhood epilepsy with centrotemporal spikesatypical benign partial epilepsy of childhoodpseudo-Lennox syndrome

Definition

A childhood-onset epilepsy that is characterized by frequent seizures of multiple types, including nocturnal focal motor and fronto-parietal opercular seizures, and daytime focal motor seizures with negative myoclonus and atypical absence seizures. Centrotemporal sharp waves are seen on EEG. During the phase of the epilepsy when seizures are frequent, neuropsychological deficits and motor impairment may be present. These deficits improve when seizures remit.