A rare epileptic encephalopathy of childhood characterized by seizures, an electroencephalographic (EEG) pattern of electrical status epilepticus in sleep (ESES) and neurocognitive regression in at least 2 domains of development. This syndrome encompasses the previous syndromes epileptic encephalopathy with continuous spike-wave in sleep and atypical childhood epilepsy with centrotemporal spikes (also previously known as pseudo-Lennox syndrome and atypical benign partial epilepsy).
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epilepsy with myoclonic atonic seizures
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febrile infection-related epilepsy syndrome
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Lennox-Gastaut syndrome
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idiopathic hemiconvulsion-hemiplegia syndrome
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GRIN2A-related developmental and/or epileptic encephalopathy with spike-wave activation in sleep
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