A sporadic form of pulmonary arterial hypertension (PAH) characterized by elevated pulmonary arterial resistance leading to right heart failure. IPAH is progressive and potentially fatal and not associated with an underlying condition or family history of PAH. The etiology is unknown.
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kyphoscoliotic heart disease
MONDO:0001492
heritable pulmonary arterial hypertension
MONDO:0017148
drug- or toxin-induced pulmonary arterial hypertension
MONDO:0017149
pulmonary veno-occlusive disease and/or pulmonary capillary haemangiomatosis
MONDO:0018554
Eisenmenger syndrome
MONDO:0019944