Pulmonary arterial hypertension (PAH) is a group of diseases characterized by mean pulmonary artery pressure >20 mmHg and elevated pulmonary arterial resistance leading to right heart failure. PAH is progressive and potentially fatal. PAH may be idiopathic and/ or familial, have overt features of venous/capillary involvement (pulmonary veno-occlusive disease, PVOD/pulmonary capillary hemangiomatosis, PCH), induced by drug or toxin (drug-or toxin-induced PAH), or associated with other diseases like congenital heart disease, connective tissue disease, HIV, schistosomiasis, portal hypertension (PAH associated with other disease).
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idiopathic pulmonary arterial hypertension
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Braddock syndrome
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chronic thromboembolic pulmonary hypertension
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hyperuricemia-pulmonary hypertension-renal failure-alkalosis syndrome
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heritable pulmonary arterial hypertension
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drug- or toxin-induced pulmonary arterial hypertension
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