Also Known As
11p partial monosomy syndromeDel(11)(p13)WAGR 11p13 deletion syndromeWAGR Syndrome/11p Deletion SyndromeWAGR syndromeWilms tumor, aniridia, genitourinary anomalies and developmental delay syndromeWilms tumor, aniridia, genitourinary anomalies and mental retardation syndrome, autosomal dominant, somatic mutationWilms tumor-aniridia-genitourinary anomalies-intellectual disability syndromeWilms tumor-aniridia-genitourinary anomalies-mental retardation syndromechromosome 11p13 deletion syndromedeletion 11p13monosomy 11p1311p deletion11p deletion syndrome11p monosomyAGR triadWAGRWAGR ComplexWilms tumor, aniridia, genitourinary anomalies, and intellectual disability syndromeWilms tumor, aniridia, genitourinary anomalies, and mental retardation syndromeWilms tumor, aniridia, genitourinary anomalies, intellectual disability syndromeWilms tumor, aniridia, genitourinary anomalies, mental retardation syndromeWilms tumor-aniridia-gonadoblastoma-intellectual disability syndromeWilms tumor-aniridia-gonadoblastoma-mental retardation syndromechromosome 11P13 deletion syndromechromosome 11p deletionchromosome 11p deletion syndromedeletion 11pmonosomy 11ppartial monosomy 11p
Definition
WAGR syndrome (Wilms tumor - aniridia - genitourinary anomalies - intellectual disability mental retardation) is a rare genetic disorder characterized by an unusual complex of congenital developmental abnormalities with intellectual disability, and an increased risk of developing Wilms tumor.