/subependymal giant cell astrocytoma

subependymal giant cell astrocytoma

Rare Disease

MONDO:0016693

Also Known As

SEGAsubependymal giant cell astrocytic neoplasmsubependymal giant cell astrocytic tumorsubependymal giant cell astrocytic tumoursubependymal giant cell astrocytoma (morphologic abnormality)

Definition

A benign, slowly growing tumor (WHO grade I) typically arising in the wall of the lateral ventricles and composed of large ganglioid astrocytes. It is the most common CNS neoplasm in patients with tuberous sclerosis complex and typically occurs during the first two decades of life. (WHO)