/hydroa vacciniforme-like lymphoma

hydroa vacciniforme-like lymphoma

Rare Disease

MONDO:0018224

Also Known As

HVLLangiocentric cutaneous T-cell lymphoma of childhoodhV-like lymphomahydroa vacciniforme-like cutaneous T-cell lymphomahydroa vacciniforme-like lymphomahydroa vacciniforme-like lymphoproliferative disorderhydroa-like cutaneous T-cell lymphoma

Definition

A rare, EBV-positive cutaneous T-cell lymphoproliferative disorder, composed of CD8 positive cytotoxic T-lymphocytes. It affects children, almost exclusively in Latin America and Asia. Patients present with papulovesicular skin lesions, clinically resembling hydroa vacciniforme, in areas of sun-exposed skin.