/maturity-onset diabetes of the young

maturity-onset diabetes of the young

Rare Disease

MONDO:0018911

Also Known As

MODYMason-type diabetesmaturity onset diabetes of the youngmaturity-onset diabetes of the youngmaturity-onset diabetes of the young (disease)Mason type diabetes

Definition

MODY (maturity-onset diabetes of the young) is a rare, familial, clinically and genetically heterogeneous form of diabetes characterized by young age of onset (generally 10-45 years of age) with maintenance of endogenous insulin production, lack of pancreatic beta-cell autoimmunity, absence of obesity and insulin resistance and extra-pancreatic manifestations in some subtypes.