Persistent left superior vena cava connecting to the left-sided atrium is a rare, congenital vascular malformation of the major vessels characterized by a persistent left superior vena cava which drains directly to the left atrium, without passing through the coronary sinus (that may be absent in some cases). Patients are usually asymptomatic and discovered incidentally, however hypoxia, cyanosis, murmurs, palpitations, cardiac structural anomalies (e.g. atrial septal defect, bicuspid aortic valve, cor triatrium) and risk of paradoxical embolization may be associated.
Comprehensive, easy-to-understand information about this condition
Checking for content...
right superior vena cava connecting to left-sided atrium
MONDO:0020441
left superior vena cava persisting to left-sided atrium
MONDO:0020442
absence of innominate vein
MONDO:0020443
subaortic course of innominate vein
MONDO:0020444
agenesis of the superior vena cava
MONDO:0020445
primary superior vena cava aneurysm
MONDO:0958097