Right superior vena cava connecting to the left-sided atrium is a rare, congenital vascular malformation of the major vessels characterized by the right SVC passing medially and dorsally to the aortic root and draining into the left atrium. Patients usually present a right-to-left systemic venous blood shunt which may manifest with arterial hypoxemia, cyanosis, exercise dyspnea, clubbing of the fingers, palpitations, murmurs and/or potentially fatal brain abscess. Association with other cardiac anomalies has been reported.
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persistent left superior vena cava connecting to the left-sided atrium
MONDO:0020440
left superior vena cava persisting to left-sided atrium
MONDO:0020442
absence of innominate vein
MONDO:0020443
subaortic course of innominate vein
MONDO:0020444
agenesis of the superior vena cava
MONDO:0020445
primary superior vena cava aneurysm
MONDO:0958097