/hand-Schuller-Christian disease

hand-Schuller-Christian disease

Rare Disease

MONDO:0020519

Also Known As

chronic multifocal Langerhans cell histiocytosisclassic multifocal Langerhans cell histiocytosishand-SChüller-Christian diseasehand-Schuller-Christian diseasemultifocal Unisystem Langerhans cell histiocytosismultifocal eosinophilic granuloma

Definition

A multifocal, unisystem form of Langerhans-cell histiocytosis. There is involvement of multiple sites in one organ system, most frequently the bone. Patients are usually young children presenting with multiple destructive bone lesions.