Also Known As
endodermal sinus neoplasm of mediastinumendodermal sinus neoplasm of the mediastinumendodermal sinus tumor of mediastinumendodermal sinus tumor of the mediastinumendodermal sinus tumour of mediastinumendodermal sinus tumour of the mediastinummediastinal endodermal sinus neoplasmmediastinal endodermal sinus tumormediastinal endodermal sinus tumourmediastinal yolk Sac neoplasmmediastinal yolk Sac tumormediastinal yolk Sac tumourmediastinum yolk sac tumormediastinum yolk sac tumouryolk Sac neoplasm of mediastinumyolk Sac neoplasm of the mediastinumyolk Sac tumor of mediastinumyolk Sac tumor of the mediastinumyolk Sac tumour of mediastinumyolk Sac tumour of the mediastinumESTmediastinal endodermal sinus tumorsmediastinal endodermal sinus tumours
Definition
An extragonadal non-seminomatous malignant germ cell tumor that arises from the mediastinum. It is characterized by the presence of small pale cells with small amount of cytoplasm and round to oval nuclei with small nucleoli forming a variety of patterns, including microcystic, macrocystic, pseudopapillary, myxomatous, hepatoid, polyvesicular vitelline, and solid. It manifests with respiratory distress, thoracic pain, fever, and superior vena cava syndrome.