/paroxysmal familial ventricular fibrillation

paroxysmal familial ventricular fibrillation

Rare Disease

MONDO:0100234

Also Known As

IVFidiopathic ventricular fibrillationidiopathic ventricular fibrillation, non Brugada typeparoxysmal familial ventricular fibrillationparoxysmal familial ventricular fibrillation (disorder)paroxysmal ventricular fibrillationventricular fibrillation, paroxysmal familial

Definition

A rare, genetic, cardiac rhythm disease characterized by ventricular fibrillation in the absence of any structural or functional heart disease, or known repolarization abnormalities. The presence of J waves is associated with a higher risk of nocturnal ventricular fibrillation events and a higher risk of recurrence.